Please use this identifier to cite or link to this item:
https://hdl.handle.net/10316/109963
DC Field | Value | Language |
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dc.contributor.author | Alfaro, T. M. | - |
dc.contributor.author | Duarte, C. | - |
dc.contributor.author | Monteiro, R. | - |
dc.contributor.author | Simão, A. | - |
dc.contributor.author | Calretas, S. | - |
dc.contributor.author | Costa, J. M. Nascimento | - |
dc.date.accessioned | 2023-11-08T15:30:42Z | - |
dc.date.available | 2023-11-08T15:30:42Z | - |
dc.date.issued | 2012 | - |
dc.identifier.issn | 08732159 | pt |
dc.identifier.uri | http://hdl.handle.net/10316/109963 | - |
dc.description.abstract | A síndromedeChurg-Strauss(SCS)éumavasculitesistémicanecrotizante,queafeta os vasosdepequenoemédiocalibreeseassociaagranulomaseosinofílicosextravasculares, eosinofilia periféricaeasma. É umasíndromerara,deetiologiadesconhecidaequeafetaambososgénerosetodosos grupos etários. Os doentescomSCSgeralmenteapresentamboarespostaàterapêuticacomglucocorticoi- des, emboraasrecidivassejamfrequentesapósasuasuspensão.Odiagnósticoeterapêutica atempada levamgeralmenteaumbomprognóstico,comumasobrevivênciade90%umano após odiagnóstico. Neste artigoéapresentadaumabreverevisãodaSCS,comparticularatenc¸ãoaodiagnóstico, terapêutica eprogressosrecentesnestaárea. De seguida,osautoresapresentamediscutemascaracterísticasclínicas,laboratoriaise imagiológicas dequatrodoentesinternadosnumServic¸odeMedicinaInternacomestediagnós- tico. Otratamentoinstituído,asrespostasobservadas eoseguimentodoscasossãotambém descritos. | pt |
dc.description.abstract | Churg-Strauss syndrome(CSS)isasystemicnecrotizingvasculitisofthesmalland medium vessels,associatedwithextravasculareosinophilicgranulomas,peripheraleosinophilia and asthma. This isararesyndromeofunknownetiology,affectingbothgendersandallagegroups. CSS patientsusuallyrespondwelltosteroidtreatment,althoughrelapsesarecommonafter it ends.Timelydiagnosisandtreatmentgenerallyleadtoagoodprognosiswitha90%survival rate atoneyear. A briefreviewofCSSispresented,withparticularattentiontodiagnosis,therapyandrecent developments inthisarea. The authorsthenreportanddiscusstheclinical,laboratoryandimagingcharacteristicsof four patientsadmittedtoanInternalMedicineDepartmentwiththisdiagnosis.Thetreatment, response andfollow-upofthecasesarealsodescribed. | pt |
dc.language.iso | eng | pt |
dc.publisher | Sociedade Portuguesa de Pneumologia | pt |
dc.rights | openAccess | pt |
dc.rights.uri | http://creativecommons.org/licenses/by-nc-nd/4.0/ | pt |
dc.subject | Síndrome de Churg-Strauss | pt |
dc.subject | Vasculite | pt |
dc.subject | Revisão | pt |
dc.subject | Casuística | pt |
dc.subject | Churg-Strauss syndrome | pt |
dc.subject | Vasculitis | pt |
dc.subject | Review | pt |
dc.subject | Case series | pt |
dc.subject.mesh | Adult | pt |
dc.subject.mesh | Female | pt |
dc.subject.mesh | Humans | pt |
dc.subject.mesh | Male | pt |
dc.subject.mesh | Middle Aged | pt |
dc.subject.mesh | Churg-Strauss Syndrome | pt |
dc.title | Churg-Strauss syndrome: case series | pt |
dc.type | article | - |
degois.publication.firstPage | 86 | pt |
degois.publication.lastPage | 92 | pt |
degois.publication.issue | 2 | pt |
degois.publication.title | Revista Portuguesa de Pneumologia | pt |
dc.peerreviewed | yes | pt |
dc.identifier.doi | 10.1016/j.rppneu.2011.12.001 | pt |
degois.publication.volume | 18 | pt |
dc.date.embargo | 2012-01-01 | * |
uc.date.periodoEmbargo | 0 | pt |
item.grantfulltext | open | - |
item.cerifentitytype | Publications | - |
item.languageiso639-1 | en | - |
item.openairetype | article | - |
item.openairecristype | http://purl.org/coar/resource_type/c_18cf | - |
item.fulltext | Com Texto completo | - |
Appears in Collections: | FMUC Medicina - Artigos em Revistas Nacionais |
Files in This Item:
File | Description | Size | Format | |
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Churg-strauss syndrome Case series.pdf | 434.07 kB | Adobe PDF | View/Open |
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This item is licensed under a Creative Commons License