Please use this identifier to cite or link to this item: https://hdl.handle.net/10316/109963
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dc.contributor.authorAlfaro, T. M.-
dc.contributor.authorDuarte, C.-
dc.contributor.authorMonteiro, R.-
dc.contributor.authorSimão, A.-
dc.contributor.authorCalretas, S.-
dc.contributor.authorCosta, J. M. Nascimento-
dc.date.accessioned2023-11-08T15:30:42Z-
dc.date.available2023-11-08T15:30:42Z-
dc.date.issued2012-
dc.identifier.issn08732159pt
dc.identifier.urihttp://hdl.handle.net/10316/109963-
dc.description.abstractA síndromedeChurg-Strauss(SCS)éumavasculitesistémicanecrotizante,queafeta os vasosdepequenoemédiocalibreeseassociaagranulomaseosinofílicosextravasculares, eosinofilia periféricaeasma. É umasíndromerara,deetiologiadesconhecidaequeafetaambososgénerosetodosos grupos etários. Os doentescomSCSgeralmenteapresentamboarespostaàterapêuticacomglucocorticoi- des, emboraasrecidivassejamfrequentesapósasuasuspensão.Odiagnósticoeterapêutica atempada levamgeralmenteaumbomprognóstico,comumasobrevivênciade90%umano após odiagnóstico. Neste artigoéapresentadaumabreverevisãodaSCS,comparticularatenc¸ãoaodiagnóstico, terapêutica eprogressosrecentesnestaárea. De seguida,osautoresapresentamediscutemascaracterísticasclínicas,laboratoriaise imagiológicas dequatrodoentesinternadosnumServic¸odeMedicinaInternacomestediagnós- tico. Otratamentoinstituído,asrespostasobservadas eoseguimentodoscasossãotambém descritos.pt
dc.description.abstractChurg-Strauss syndrome(CSS)isasystemicnecrotizingvasculitisofthesmalland medium vessels,associatedwithextravasculareosinophilicgranulomas,peripheraleosinophilia and asthma. This isararesyndromeofunknownetiology,affectingbothgendersandallagegroups. CSS patientsusuallyrespondwelltosteroidtreatment,althoughrelapsesarecommonafter it ends.Timelydiagnosisandtreatmentgenerallyleadtoagoodprognosiswitha90%survival rate atoneyear. A briefreviewofCSSispresented,withparticularattentiontodiagnosis,therapyandrecent developments inthisarea. The authorsthenreportanddiscusstheclinical,laboratoryandimagingcharacteristicsof four patientsadmittedtoanInternalMedicineDepartmentwiththisdiagnosis.Thetreatment, response andfollow-upofthecasesarealsodescribed.pt
dc.language.isoengpt
dc.publisherSociedade Portuguesa de Pneumologiapt
dc.rightsopenAccesspt
dc.rights.urihttp://creativecommons.org/licenses/by-nc-nd/4.0/pt
dc.subjectSíndrome de Churg-Strausspt
dc.subjectVasculitept
dc.subjectRevisãopt
dc.subjectCasuísticapt
dc.subjectChurg-Strauss syndromept
dc.subjectVasculitispt
dc.subjectReviewpt
dc.subjectCase seriespt
dc.subject.meshAdultpt
dc.subject.meshFemalept
dc.subject.meshHumanspt
dc.subject.meshMalept
dc.subject.meshMiddle Agedpt
dc.subject.meshChurg-Strauss Syndromept
dc.titleChurg-Strauss syndrome: case seriespt
dc.typearticle-
degois.publication.firstPage86pt
degois.publication.lastPage92pt
degois.publication.issue2pt
degois.publication.titleRevista Portuguesa de Pneumologiapt
dc.peerreviewedyespt
dc.identifier.doi10.1016/j.rppneu.2011.12.001pt
degois.publication.volume18pt
dc.date.embargo2012-01-01*
uc.date.periodoEmbargo0pt
item.grantfulltextopen-
item.cerifentitytypePublications-
item.languageiso639-1en-
item.openairetypearticle-
item.openairecristypehttp://purl.org/coar/resource_type/c_18cf-
item.fulltextCom Texto completo-
Appears in Collections:FMUC Medicina - Artigos em Revistas Nacionais
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